Lutembacher Syndrome- A Case Report and Reappraisal

Lutembacher syndrome is defined as a combination of mitral stenosis (mostly rheumatic) with a left to right shunt at the atrial septal level. It is a rare disease with a higher prevalence in areas, where rheumatic heart disease is common. Diagnosis on physical examination can be challenging and therefore echocardiography is generally required to make the diagnosis. If not diagnosed and treated early, patient may develop right heart failure and arrhythmic complications, which bear a bad prognosis. We present a case-based reappraisal of Lutembacher syndrome in a 23-years old female, who presented with symptoms of pulmonary hypertension and heart failure.