Juvenile Myofibromatosis of Mandible- A Case Report

Myofibroma is a solitary benign tumor of myofibroblasts. Myofibromatosis describes multiple, simultaneous myofibromas at different sites in various organs. Myofibromatosis is a rare but well recognized entity which was originally thought to affect only neonates and infants. It is now apparent however that adults may also be affected. Solitary cases affecting the oral cavity appear to be rare. This case report documents a case of myofibromatosis in a 13-year-old boy. The elongated spindle cells were identified as myofibroblasts by immunohistochemistry. The lesions showed characteristic features which enabled them to be distinguished from other fibrous lesions and from benign or malignant smooth muscle tumors with which they have been often confused.