Cleidocranial Dysostosis - A Case Report

Cleidocranial dysplasia (CCD) is a rare autosomal dominant disorder that exhibits several skeletaldefects and dental abnormalities.The characteristic features seen in cleidocranial dysplasia are aplastic or hypoplastic clavicles,delayedclosureor open fontanelles, open skull sutures and dental abnormalities, which includes over retention of primary dentition and delayed eruption of permanent dentition, with presence of multiple impacted supernumerary teeth. In this article we report 2 cases of cleidocranial dysplasia reported in our dental outpatient department with an aim to highlight the clinical features,dental abnormalities and radiological features.