DOEGE-POTTER Syndrome in Malignant Neurofibromatous Tumor: A Case Report |Biomedgrid

DOEGE-POTTER syndrome is a paraneoplastic syndrome in which hypoglycemia results from tumors producing insulin-like growth factor (IGFII). It is most often the solitary fibrous tumor of the pleura. These are rare and may be discovered incidentally, during non-specific respiratory symptoms or during hypoglycemia. Hypoglycemia occurs in large tumors and disappears after surgery, which is the treatment of choice, allowing permanent cure in the majority of cases.