MULTIPLE INTRACRANIAL MYELOID SARCOMAS- A CASE REPORT

We report unusual case of 4 year old female child with right orbital swelling, right cerebellar space occupying(SOL) lesion, midline frontal SOL and hydrocephalus. Initially, right ventriculo peritoneal(VP) shunt and biopsy from the orbital swelling done ,which was reported as non-Hodgkins lymphoma(NHL) but IHC and further haematological evaluations were found to be negative for NHL.As patient deteriorated further because of posterior fossa SOL, occipital craniectomy and total excision of posterior fossa SOL done. Now the biopsy was reported as myeloid sarcoma with positive CD 117 and myeloperoxidase and on examining the blood and bone marrow it was found that she was having Acute Myeloid Leukaemia (AML) M 2 type. Myeloid sarcoma itself is a rare tumour. In this case it is multiple. Multiple intra cranial myeloid sarcomas are even rare among all reported cases.