HEREDITARY SENSORY AND AUTONOMIC NEUROPATHY - A CASE REPORT

The hereditary sensory and autonomic neuropathies (HSAN) are a group of rare disorders characterized by prominent sensory and autonomic neuropathy without motor involvement. This case report describes a 20 year old male who had progressive auto amputation of right leg and great toe of the left leg with acral mutilation of the fingers. This case is presented to highlight the progressive nature of the disease, importance of early diagnosis in preventing the complications, rarity of the disease itself and scope for future research.