A Rare Case of Nonbullous Congenital Ichthyosiform Erythroderma in a Preterm Neonate - A Case Report

Nonbullous congenital ichthyosiform erythroderma (NBCIE) is a rare non blistering disorder and one form of severe congenital ichthyosis. The incidence is 1 in 300, 000 individuals of all races. An affected newborn is usually born as a collodion baby. It presents with fine grey white scales after shedding of the collodion membrane. Here we report one such rare case of NBCIE, diagnosed in a preterm neonate at 3 weeks of age with consistent clinical and skin biopsy findings.