A Rare Case of Malignant Peripheral Nerve Sheath Tumour

Malignant peripheral nerve sheath tumor (MPNST) is a rare variety of soft tissue sarcoma of ectomesenchymal origin. World Health organization (WHO) coined the term MPNST replacing previous terminology, such as malignant schwannoma, malignant neurilemmoma, and neurofibrosarcoma. It has an incidence of 1 per 1, 00, 000 population and which constitutes between 3 to 10 % of all soft tissue sarcomas. A solitary MPNST without neurofibromatosis is rarity and a MPNST arising from a small nerve ending is also rarity.