ResearchBib Share Your Research, Maximize Your Social Impacts
Sign for Notice Everyday Sign up >> Login

Multiple Stromal Tumors in Von Recklinghausen Disease: A Real Diagnostic and Therapeutic Challenge

Journal: International Journal of Science and Research (IJSR) (Vol.11, No. 4)

Publication Date:

Authors : ; ; ; ; ;

Page : 25-27

Keywords : Gastrointestinal stromal tumours; Von Recklinghausen disease; therapeutic challenge;

Source : Downloadexternal Find it from : Google Scholarexternal


Gastrointestinal stromal tumours (GIST) are rare. They usually occur sporadically, or may be part of a pathological framework such as Neurofibromatosis type 1, and Carney's triad. Familial forms exist. GISTs associated with Neurofibromatosis Type 1 differ from sporadic GISTs in terms of epidemiology, clinical, immunohistochemical, molecular biology, prognosis, and therapeutic management. We report the case of a patient with multiple GISTs in relation to Neurofibromatosis type 1, with the aim of outlining the diagnostic and therapeutic difficulties through a review of the literature.

Last modified: 2022-05-14 21:04:25