A Case Report of Orbital IgG4 Related Disease

IgG4 related disease is an uncommon systemic disorder which involves almost all organs in the body with characteristic fibrosis. The characteristic features are chronic non inflammatory lid swelling and proptosis. The term systemic condition IgG4-related disease, which is characterised by lymphocyte infiltration, plasma cell infiltration and consequent fibrosis in affected areas, is IgG4-related ophthalmic disease (IgG4-ROD). Systemic steroids are used as first line to decrease the lesion size, but relapse are more common after discontinuation