Dermatofibrosarcoma Infiltrating the Parotid Gland: Case Report and Literature Review

Introduction: Primary dermatofibrosarcoma protuberans (DFSP) of the salivary gland is extremely rare. Case Presentation: A 37-year-old female complained of a 5-year, slowgrowing lump in the right parotid region without any other sign or symptom. At examination there was a firm, non-movable nodule on the right parotid gland. The ultrasound/Doppler showed a well-vascularized solid nodule with ill-defined borders on the inferior edge of the parotid. A total parotidectomy was performed. Sections revealed an ill-defined, non-encapsulated nodule measuring 2.5 x 2.0 x 1.3 cm. The histopathological diagnosis coupled with immunohistochemistry was consistent with DFSP. Conclusion: We report a rare case of DFSP infiltrating the parotid gland. Whether it represents a primary lesion or a subcutaneous tumor infiltrating the parotid gland, this tumor presented clinically as a parotid lump and diffusely infiltrated this gland. Treatment modalities and prognosis are not well-defined due to the scarcity of cases described in the literature.