A RARE CASE OF EVANS SYNDROME

Evans syndrome is a very rare autoimmune disorder in which the immune system destroys the bodys red blood cells, white blood cells and platelets. Affected people often experience thrombocytopenia and coombs positive haemolytic anaemia. Here we report a case of 12 years old girl presented with fever for 15 days with severe anaemia and thrombocytopenia. Later on, the child developed hemoglobinuria, malena, diffuse rash and hepatosplenomegaly. Her investigations revealed positive direct coombs test, ANA, anti ds DNA. So, the diagnosis of Evans syndrome was made.