IgG4 Related Disease of the Paratestis

IgG4 related disease (IgG4-RD) is characterized by tumefaction or infiltration of the tissue by IgG4 positive plasma cells and increased serum IgG4 levels. It affects various organs like pancreas, submandibular glands, thyroid, lungs, pituitary, retroperitoneal tissue, kidney and the prostate. IgG4D in the paratesticular region is rare and only a few cases have been reported so far. Here we report a case of IgG4-RD which presented as a pseudotumor in the left paratesticular region.