Evans-Fisher syndrome. Report of a case

A case of female, 4 years old, urban area, with a history of presenting during eight months immune and purpura thrombocytopenic after upper respiratory infection began with purpuric manifestations in the form of petechiae and bruises scattered throughout the body, severe skin pale mucosa, with both clinical expression of thrombocytopenia and severe anemia, hepatomegaly of 2 and 4 cm splenomegaly generalized peripheral lymphadenopathy small to medium size, skin and sclera jaundice, dark urine, too. Haematological humoral and immunological studies were performed. It is served in the Intermediate Care Unit of the hospital, evolved favorably with satisfactory response to steroid treatment. Diagnostic case discussion confirmed diagnosis of Evans-Fisher syndrome, reviewing the updated bibliography of this entity.